MSUD product journey

Please note:

  • All of the products below are Foods for Special Medical Purposes and must be used under medical supervision.
  • Availability of products vary from country to country. Please contact your healthcare professional or local Nutricia contact for more information which products are available in your region.

GA1 Product Journey

When an infant is diagnosed with Glutaric Aciduria Type 1 (GA1) Anamix Infant is the first introduction to the nutritional solutions provided by Nutricia Metabolics.

At every stage in life, we are there with products and services to support the dietary management of GA1.

TYR Anamix infant

GA1 Anamix infant

For use in infants from birth to 12 months and as a supplementary feed up to 3 years.

For the dietary management of proven glutaric aciduria type 1. An amino acid based lysine-free, low tryptophan powdered formulation containing essential and non-essential amino acids, carbohydrate, fat, fibre, vitamins, minerals and trace elements.

  • Only infant feed for metabolic conditions that contains the prebiotic fibre blend scGOS:IcFOS (9:1)*1
  • Convenient and easy to use
  • Developed to comply with the highest quality and food safety standards2
  • Available in a 400g can

Ingredients:  Glucose syrup, vegetable oils (high oleic sunflower oil, coconut oil, rapeseed oil, sunflower oil), galacto-oligosaccharides (from cow's milk), L-leucine, L-glutamic acid, L-proline, L-arginine, L-valine, L-isoleucine, glycine, emulsifier (citric acid esters of mono- and diglycerides of fatty acids), L-aspartic acid, calcium phosphate, L-threonine, L-tyrosine, L-phenylalanine, L-serine, L-histidine, L-alanine, potassium citrate, fructo-oligosaccharides, potassium chloride, L-cystine, choline bitartrate, magnesium acetate, calcium glycerophosphate, sodium hydrogen phosphate, L-methionine, oil from Crypthecodinium cohnii, oil from Mortierella alpina, sodium chloride, L-glutamine, inositol, L-tryptophan, L-ascorbic acid, antioxidants (sunflower lecithin, ascorbyl palmitate), taurine, ferrous sulphate, zinc sulphate, L-carnitine, DL-α tocopheryl acetate, calcium D-pantothenate, nicotinamide, copper sulphate, thiamin hydrochloride, pyridoxine hydrochloride, riboflavin, retinyl acetate, potassium iodide, manganese sulphate, pteroylmonoglutamic acid, chromium chloride, phytomenadione, sodium selenite, sodium molybdate, D-biotin, cholecalciferol, cyanocobalamin.

Allergens: Cow's milk

As a child grows their nutritional needs also change

GA1 Anamix junior

Adapted to the changing needs of a growing child and designed to taste great.***

For use in children 1 to 10 years of age.

For the dietary management of proven glutaric aciduria type 1 (GA1). A lysine-free, low tryptophan powder drink mix containing a balanced mix of the other essential and non-essential amino acids, carbohydrate, fat (including docosahexaenoic acid (DHA)), vitamins, minerals, trace elements and fibre.

  • The only protein substitute for 1 to 10 year olds with added fibre
  • Contains a unique fibre blend to support gut health3-8.
  • GA1 Anamix Junior powder is available in neutral flavour to help transition from Anamix Infant.
  • Available in a 400g can and convenient 18g sachets for on-the-go use.

Ingredients:  Dried glucose syrup, dietary fibres (oligofructose, inulin, resistant starch, cellulose, acacia gum, soy polysaccharides), refined vegetable oils (high oleic sunflower, canola, medium chain triglycerides (palm kernel and/or coconut oil), sunflower), L-leucine, calcium phosphate dibasic, L-glutamine, L-proline, L-arginine, L-valine, L-isoleucine, glycine, flavouring, magnesium L-aspartate, L-threonine, L-tyrosine, L-phenylalanine, L-serine, tri potassium citrate, L-alanine, L-histidine, tri sodium citrate, L-cystine, maltodextrin, choline bitartrate, calcium chloride, L-methionine, emulsifiers (E472c, sunflower lecithin), L-aspartic acid, high docosahexaenoic acid oil from Crypthecodinium cohnii, sodium chloride, L-tryptophan, L-ascorbic acid, M-inositol, taurine, ferrous sulphate, L-carnitine, zinc sulphate, DL-α-tocopheryl acetate, nicotinamide, calcium D-pantothenate, manganese sulphate, copper sulphate, thiamin hydrochloride, pyridoxine hydrochloride, riboflavin, vitamin A acetate, antioxidants (E304(i), E306, E307), folic acid, potassium iodide, sodium molybdate, sodium selenite, chromium chloride, vitamin D3, vitamin K1, D-biotin, cyanocobalamin.
Allergens: Soy

TYR Anamix junior range

Continue dietary management with GA1 MAXAMUM, an energy-dense protein substitute

TYR Maxamum

GA1 Maxamum / XLYS LOW TRY Maxamum

GA1 Maxamum is an energy-dense protein substitute that can be concentrated.

Suitable for children from 8 years of age, teenagers, and adults, including pregnant women (in conjunction with standard folic acid supplementation).

  • High in energy and low in fat protein substitute to meet more complex nutritional needs.
  • A lysine-free, low tryptophan powdered mixture of amino acids with carbohydrate, vitamins, minerals and trace elements.
  • Available in a 500g can.

Ingredients: Dried glucose syrup, L-leucine, L-glutamic acid, L-proline, L-arginine, L-valine, calcium glycerophosphate, glycine, L-isoleucine, L-aspartic acid, L-threonine, L-tyrosine, L-phenylalanine, L-serine, L-alanine, L-histidine, tri potassium citrate, L-cystine, magnesium hydrogen phosphate, sodium chloride, L-methionine, tri sodium citrate, sugar, choline bitartrate, emulsifier (soy lecithin), magnesium acetate, L-glutamine, L-tryptophan, taurine, tri calcium phosphate, ferrous sulphate, L-ascorbic acid, inositol, zinc sulphate, L-carnitine, nicotinamide, manganese sulphate, DL-α-tocopheryl acetate, calcium D-pantothenate, copper sulphate, pyridoxine hydrochloride, thiamin hydrochloride, riboflavin, vitamin A acetate, folic acid, chromium sulphate, sodium molybdate, potassium iodide, D-biotin, sodium hydrogen selenite, vitamin K1, vitamin D3, cyanocobalamin.
Allergens: Soy

Other Essentials

We offer other essential products to personalise the dietary management of GA1 to meet specific daily nutritional requirements or as part of an individually tailored emergency regime as appropriate.

XLYS TRY Glutaridon

XLYS TRY Glutaridon is a concentrated source of protein to meet extra requirements in infants, children and adults.
  • Mix with usual daily protein substitute or use on its own.
  • A lysine-free, low tryptophan mixture of essential and non-essential amino acids.
  • May be given in a concentrated form, e.g., a paste or concentrated drink. Can also be added to other low-protein drinks.
  • Available in a 500 g can

Ingredients: L-leucine, L-glutamic acid, L-proline, L-arginine, L-valine, L-isoleucine, glycine, L-aspartic acid, L-threonine, L-tyrosine, L-phenylalanine, L-serine, dried glucose syrup, L-alanine, L-histidine, L-cystine, L-methionine, L-glutamine, tricalcium phosphate, taurine, L-carnitine.
Allergens: N/A

XPHEN TYR Tyrosidon
TYR GMPRO Mix-In

L-Carnitine

To tailor nutritional intake to meet individual requirements as part of the integral management of GA1.
  • Suitable from birth to meet individual requirements.
  • A powdered 100% pure FSMP grade form of the amino acid L-Carnitine
  • Recommended for lifelong supplementation in the dietary management of GA19

Ingredients: L-carnitine
Allergens: N/A

Energivit

For infants and children requiring additional energy and micronutrients on a protein-restricted diet.

Suitable for infants and children

For the dietary management of conditions where protein intake is restricted or where additional energy, vitamins, minerals and trace elements are required. A protein-free powdered mixture of carbohydrate, fat, vitamins, minerals, and trace elements.

Gives flexibility to cater to patient's individual energy, vitamins and minerals requirements.

  • Suitable for bottle, tube and sip feeding
  • Available in a 400g can

Ingredients: Glucose syrup, vegetable oils (high oleic sunflower oil, coconut oil, rapeseed oil, sunflower oil), emulsifier (citric acid esters of mono- and diglycerides of fatty acids), tri calcium phosphate, potassium citrate, potassium chloride, choline bitartrate, magnesium acetate, calcium glycerophosphate, sodium hydrogen phosphate, oil from Crypthecodinium cohnii, oil from Mortierella alpina, sodium chloride, inositol, L-ascorbic acid, antioxidants (sunflower lecithin, ascorbyl palmitate), ferrous sulphate, zinc sulphate, nicotinamide, DL-α-tocopheryl acetate, calcium D-pantothenate, copper sulphate, thiamin hydrochloride, pyridoxine hydrochloride, riboflavin, retinyl acetate, potassium iodide, manganese sulphate, pteroylmonoglutamic acid, chromium chloride, phytomenadione, sodium selenite, sodium molybdate, D-biotin, cholecalciferol, cyanocobalamin.
Allergens: N/A

Energivit
TYR GMPRO Mix-In

Super Soluble Duocal

A powder consisting only of a balanced blend of fats and carbohydrates.

Suitable for infants, children and adults.

A powder consisting of a balanced blend of fat and carbohydrate. Milk protein free. Can be used as part of a patients' emergency regime or to meet increased energy requirements in general.

  • Enables you to tailor to your patient's individual energy requirements.
  • Available in a 400g can

Ingredients: Dried glucose syrup, medium chain triglycerides (palm kernal and/ or coconut oil), safflower oil, canola oil, emulsifier (E472(c))
Allergens: N/A

Super Soluble Maxijul

A powdered neutral-flavoured carbohydrate energy source.

Suitable for infants, children and adults.

A powdered carbohydrate energy supplement derived from the hydrolysis of corn starch to produce a glucose polymer of approximately five glucose units. Forms an integral part of a patient’s emergency regime whereby individual energy requirements can be exactly matched.

Super Soluble Maxijul can also be used to meet increased energy requirements in general:

  • Flexible to mix with existing protein substitutes, low-protein sweet or savoury foods and low-protein hot or cold drinks.
  • Available in 200g can

Ingredients: Dried glucose syrup, medium chain triglycerides (palm kernel and/or coconut oil), safflower oil, canola oil, emulsifier (E472(c)).
Allergens: N/A

Super Soluble Maxijul
Flavour sachets

Flavour sachets

To add variety and aid adherence for use in combination with our neutral flavoured powdered protein substitutes.

A Grapefruit flavoured powder consisting of mixture of citric acid and flavouring. With sweetener.
A Lemon-Lime flavoured powder consisting of mixture of citric acid, flavouring and colour. With sweetener.
A Cherry-Vanilla flavoured powder consisting of mixture of malic acid, flavouring and colour. With sugar and sweetener.

Suitable for use with a range of unflavoured amino acid and peptide-based foods for special medical purposes

  • Offer variety with 3 ready to mix flavours: Cherry-Vanilla, Lemon-Lime and Grapefruit
  • Available in a box of 20 x 5g sachets
  • Contains a carbohydrate base with sugars and sweeteners

Ingredients: 
Grapefruit flavour: Flavour enhancer (citric acid), flavouring (32%), sweetener (acesulfame-K).
Lemon-Lime flavour: Flavour enhancer (citric acid), flavouring (31%), sweetener (acesulfame-K), colour (carotenes).
Cherry-Vanilla flavour: Flavourings (40%), flavour enhancer (malic acid), colour (betanin), glucose syrup, sweetener (acesulfame-K).
Allergens: N/A

Loprofin Range

Low protein kitchen essentials that can be used in any rare disorder of protein metabolism to provide additional energy and increase variety and flavour in low-protein diets.

Combine Loprofin kitchen essentials with local and globally created recipes to prepare tasty meals and snacks from breakfast to dinner.

Find out more

Inherited Metabolic Disorders

Inherited metabolic disorders (IMDs), also known as Inborn errors of metabolism (IEM) are a group of rare disorders caused by genetic defects.

Find out more

Learn more about latest research

News article about recent systematic review and meta-analysis exploring why protein substitutes are still very relevant to patients with PKU on BH4 treatment.

Find out more

* A blend researched and designed by Nutricia as part of the development of nutrition for healthy infants and similar to oligosaccharides in breast milk.

* As compared to other iFSMPs in the UK market, MIMS Nov 2020

*** Taste testing carried out with patients with IMD, data on file; 2017

  1. Moro G and Boehm H. Functional Food Review 2012; 4:1-12 - as compared to other iFSMPs in the UK market, MIMS Nov 2020
  2. Nutricia products are manufactured to conform with food industry good manufacturing practices as described in the FSSC 22000 standard.
  3. Trier E et al. JPGN 1999;28(5):595
  4. Evans S et al. J Hum Nutr Diet 2009;22:414-421
  5. Hofman Z et al. Clin Nutr 2001;20(S3)217A:P63
  6. Daly A et al. J Hum Nutr Diet 2004;17:365–70.
  7. Guimber D et al. J Pediatr Gastroenterol Nutr 2007;44e201 (PN1–15).
  8. Grogan J et al. J Hum Nutr Diet 2006; 19:458–477
  9. Boy N et al. Recommendations for diagnosing and managing individuals with glutaric aciduria type 1: Third revision. J Inherit Metab Dis. 2023 May;46(3):482-519. doi: 10.1002/jimd.12566. Epub 2022 Nov 17. PMID: 36221165

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